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Конфетті-подібна макулярна атрофія

ORPHA:221142· ICD-10 L90.8· Confetti-like macular atrophy

Визначення(English summary)

A rare, acquired, dermis elastic tissue disorder with decreased elastic tissue characterized by multiple, asymptomatic, well demarcated, flat, hypopigmented atrophic macular skin lesions distributed over upper trunk and proximal upper limbs. Histopathological examination reveals atrophic epidermis with decreased basal pigmentation, perivascular mononuclear infiltration in the upper dermis, and disorganized, hyalinized, coarse collagen bundles, and variable loss of elastic fibers in the dermis.

Поширеність
<1 / 1 000 000
Вік початку
Adult