Сімейна ізольована дилатаційна кардіоміопатія
ORPHA:154· ICD-10 I42.0· Familial isolated dilated cardiomyopathy
Визначення(English summary)
A rare familial cardiomyopathy characterized by the dilation of left ventricle and progressively impairing of systolic ventricular function, in the absence of abnormal loading conditions or coronary artery disease sufficient to cause global systolic impairment. The disease may cause heart failure or arrhythmia. The disease is isolated when no additional atypical cardiac or extracardiac manifestations are present.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Autosomal dominant, Autosomal recessive, Mitochondrial inheritance, X-linked recessive
- Вік початку
- All ages