Первинний ангііт центральної нервової системи
ORPHA:140989· ICD-10 I67.7· Primary angiitis of the central nervous system
Визначення(English summary)
A rare, medium or small vessel vasculitis characterized by focal and/or diffuse neurologic symptoms due to a documented arteritic process in the central nervous system, in the absence of other identified underlying cause (infectious, systemic, other neurologic diseases, etc.). It presents with non-specific symptoms of headache, stroke or transient ischemic attacks with cognitive impairment, hemiplegia, weakness, and rarely, with cranial nerve involvement, seizures and ataxia.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- All ages