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Haddad syndrome

ORPHA:99803· ICD-10 G47.3

Definition

Haddad syndrome is a rare congenital disorder in which congenital central hypoventilation syndrome (CCHS), or Ondine syndrome, occurs concurrently with Hirschsprung disease.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant, Multigenic/multifactorial
Age of onset
Infancy, Neonatal