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Hereditary continuous muscle fiber activity

ORPHA:972· ICD-10 G71.1

Definition

Hereditary continuous muscle fiber activity is a rare, non-dystrophic myopathy characterized by generalized myokymia and increased muscle tone associated with delayed motor milestones, leg stiffness, spastic gait, hyperreflexia and Babinski sign. Symptoms may be worsened by febrile illness or anesthesia.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Childhood, Infancy