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Isolated thyroid-stimulating hormone deficiency

ORPHA:90674· ICD-10 E03.1

Definition

A type of central congenital hypothyroidism, a permanent thyroid deficiency that is present from birth, characterized by low levels of thyroid hormones due to a deficiency in TSH synthesis.

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal