Hereditary progressive cardiac conduction defect
ORPHA:871· ICD-10 I45.8
Definition
A genetic cardiac rhythm disease that may progress to complete atrioventricular (AV) block. The disease is either asymptomatic or manifests as dyspnea, dizziness, syncope, abdominal pain, heart failure or sudden death.
- Prevalence
- Unknown
- Inheritance
- Autosomal dominant
- Age of onset
- Adult