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Saethre-Chotzen syndrome

ORPHA:794· ICD-10 Q87.0

Definition

A syndrome characterized by unilateral or bilateral coronal synostosis, facial asymmetry, ptosis, strabismus and small ears with prominent superior and/or inferior crus, among other less common manifestations.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant
Age of onset
Antenatal, Neonatal