Diazoxide-resistant focal hyperinsulinism
ORPHA:79298
Definition
A form of congenital diazoxide-resistant hyperinsulinism characterized by recurrent episodes of profound hypoglycemia caused by an excessive/uncontrolled insulin secretion (inappropriate for the level of glycemia) due to a focal adenomatous hyperplasia of pancreas, that is unresponsive to medical treatment with diazoxide.
- Prevalence
- Unknown
- Age of onset
- All ages