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Alpha-N-acetylgalactosaminidase deficiency type 2

ORPHA:79280· ICD-10 E77.1

Definition

A very rare mild adult type of NAGA deficiency with the features of angiokeratoma corporis diffusum and mild sensory neuropathy.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Adult