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Acrocapitofemoral dysplasia

ORPHA:63446· ICD-10 Q78.8

Definition

A rare skeletal dysplasia, characterized clinically by short stature of variable degrees with short limbs, brachydactyly and narrow thorax.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal