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Progressive myoclonic epilepsy type 7

ORPHA:435438· ICD-10 G40.3

Definition

A rare, genetic, neurological disorder characterized by childhood to adolescent onset of progressive myoclonus (which becomes very severe and results in major motor impediment) associated with infrequent tonic-clonic seizures, and, occasionally, ataxia. Learning disability prior to seizure onset and mild cognitive decline may be associated.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Childhood