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Neonatal severe primary hyperparathyroidism

ORPHA:417· ICD-10 E21.0

Definition

Neonatal severe primary hyperparathyroidism (NSHPT) is characterized by severe hypercalcemia (> 3.5 mM) from birth and associated with major hyperparathyroidism.

Prevalence
Unknown
Inheritance
Autosomal recessive, Not applicable
Age of onset
Neonatal