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Trisomy 13 syndrome

ORPHA:3378· ICD-10 Q91.4

Definition

A rare chromosomal anomaly characterized by the presence of extra chromosome 13 material and manifesting with severe intellectual disability and multiple congenital anomalies including holoprosencephaly, microcephaly, microphthalmia, scalp defect, cleft lip/palate, congenital heart defects, and postaxial polydactyly. Neurological involvement may lead to seizures and hypotonia.

Prevalence
1-9 / 100 000
Inheritance
Not applicable, Unknown
Age of onset
Antenatal, Neonatal