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Deaf blind hypopigmentation syndrome, Yemenite type

ORPHA:3214· ICD-10 Q13.8

Definition

Yemenite deaf-blind hypopigmentation syndrome is an exceedingly rare genetic disorder characterized by cutaneous pigmentation anomalies, ocular disorders and hearing loss.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Infancy, Neonatal