vitalwiki

Machado-Joseph disease type 1

ORPHA:276238· ICD-10 G11.8

Definition

Machado-Joseph disease type 1 is a rare, usually severe subtype of Machado-Joseph disease (SCA3/MJD) characterized by the presence of marked pyramidal and extrapyramidal signs.

Prevalence
Unknown
Inheritance
Autosomal dominant
Age of onset
Adult, Childhood