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Congenital muscular dystrophy, Fukuyama type

ORPHA:272· ICD-10 G71.0

Definition

A rare congenital progressive muscular dystrophy often characterized by brain malformation (cobblestone lissencephaly), dystrophic changes in skeletal muscle, severe intellectual deficit, epilepsy and motor impairment.

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Infancy