vitalwiki

Hyposmia-nasal and ocular hypoplasia-hypogonadotropic hypogonadism syndrome

ORPHA:2250· ICD-10 Q87.0

Definition

This syndrome is characterized by the association of severe nasal hypoplasia, hypoplasia of the eyes, hyposmia, hypogeusia and hypogonadotropic hypogonadism.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant, Unknown
Age of onset
Antenatal, Neonatal