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Holoprosencephaly-postaxial polydactyly syndrome

ORPHA:2166· ICD-10 Q87.8

Definition

Holoprosencephaly-postaxial polydactyly syndrome associates, in chromosomally normal neonates, holoprosencephaly, severe facial dysmorphism, postaxial polydactyly and other congenital abnormalities, suggestive of trisomy 13.

Prevalence
Unknown
Inheritance
Autosomal recessive
Age of onset
Antenatal, Neonatal