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Craniodigital-intellectual disability syndrome

ORPHA:1514· ICD-10 Q87.0

Definition

Craniodigital syndrome - intellectual deficit is characterised by syndactyly of the fingers and toes, characteristic facies (`startled' facial expression with a small pointed nose, micrognathia, long dark eyelashes and prominent eyebrows) and intellectual deficit.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive, X-linked recessive
Age of onset
Neonatal