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Aphalangy-syndactyly-microcephaly syndrome

ORPHA:1113· ICD-10 Q87.2

Definition

An extremely rare malformation syndrome characterized by the association of partial distal aphalangia with syndactyly, duplication of metatarsal IV, microcephaly, and mild intellectual disability.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Antenatal, Neonatal