vitalwiki

Неамілоїдна фібрилярна гломерулопатія

ORPHA:97566· ICD-10 N03.6· Non-amyloid fibrillary glomerulopathy

Визначення(English summary)

Non-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy (ITG, see this term) are often grouped together as pathogenetically related diseases.

Успадкування
Not applicable
Вік початку
Adult