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Паукоімунний гломерулонефрит

ORPHA:93126· ICD-10 N05.7· Pauci-immune glomerulonephritis

Визначення(English summary)

A rare small vessel vasculitis associated with rapidly progressive glomerulonephritis (GN) and clinically characterized by renal manifestations such as urinary abnormalities (hematuria and/or proteinuria) and hypertension leading to renal failure within days or weeks, and distinguished by the absence of immune deposits on immunofluorescent microscopy. The disease can occur as a renal-limited disease or as a component of systemic necrotizing small-vessel vasculitis.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adolescent, Adult, Childhood, Elderly