Паукоімунний гломерулонефрит
ORPHA:93126· ICD-10 N05.7· Pauci-immune glomerulonephritis
Визначення(English summary)
A rare small vessel vasculitis associated with rapidly progressive glomerulonephritis (GN) and clinically characterized by renal manifestations such as urinary abnormalities (hematuria and/or proteinuria) and hypertension leading to renal failure within days or weeks, and distinguished by the absence of immune deposits on immunofluorescent microscopy. The disease can occur as a renal-limited disease or as a component of systemic necrotizing small-vessel vasculitis.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- Adolescent, Adult, Childhood, Elderly