vitalwiki

Синдром Таунса-Брокса

ORPHA:857· ICD-10 Q87.8· Townes-Brocks syndrome

Визначення(English summary)

A rare genetic disorder characterized by the triad of imperforate anus, dysplastic ears often associated with sensorineural and/or conductive hearing impairment, and thumb malformations. These features are often associated with other signs mainly affecting the kidneys and heart.

Поширеність
1-9 / 1 000 000
Успадкування
Autosomal dominant
Вік початку
All ages