vitalwiki

Хронічна тромбоемболічна легенева гіпертензія

ORPHA:70591· ICD-10 I26.0· Chronic thromboembolic pulmonary hypertension

Визначення(English summary)

A rare complication of acute pulmonary embolism (PE), either symptomatic or not, that is characterized by fibrotic intravascular material occlusion of pulmonary arteries in combination with a secondary microvasculopathy of vessels less than 500 µm. The consequence is an increase in pulmonary vascular resistance (PVR) and progressive right heart failure.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
Adolescent, Adult, Elderly