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ORPHA:64741· ICD-10 C34.2· Pulmonary blastoma
Визначення(English summary)
A biphasic primary lung neoplasm, belonging to the group of sarcomatoid lung carcinomas (SLCs). The tumor contains both an epithelial well-differentiated component, showing tubular architecture resembling the normal fetal lung, and a mesenchymal undifferentiated stroma with a so-called ''blastema-like'' configuration that resembles an embryonic lung.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Multigenic/multifactorial
- Вік початку
- Adult