Pulmonary blastoma
ORPHA:64741· ICD-10 C34.2
Definition
A biphasic primary lung neoplasm, belonging to the group of sarcomatoid lung carcinomas (SLCs). The tumor contains both an epithelial well-differentiated component, showing tubular architecture resembling the normal fetal lung, and a mesenchymal undifferentiated stroma with a so-called ''blastema-like'' configuration that resembles an embryonic lung.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Multigenic/multifactorial
- Age of onset
- Adult