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Pulmonary blastoma

ORPHA:64741· ICD-10 C34.2

Definition

A biphasic primary lung neoplasm, belonging to the group of sarcomatoid lung carcinomas (SLCs). The tumor contains both an epithelial well-differentiated component, showing tubular architecture resembling the normal fetal lung, and a mesenchymal undifferentiated stroma with a so-called ''blastema-like'' configuration that resembles an embryonic lung.

Prevalence
<1 / 1 000 000
Inheritance
Multigenic/multifactorial
Age of onset
Adult