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Неонатальний дистрес-синдром новонароджених

ORPHA:641829· ICD-10 P01.8· Neonatal compartment syndrome

Визначення(English summary)

A rare non-inflammatory vasculopathy characterized by intracompartmental pressure typically in a distal upper extremity due to intrauterine ischemia and external compression. Affected limb presents significant swelling and sentinel skin changes (desquamation, blister/bullae formation, and skin necrosis). It can lead to long-term sequelae including Volkmann contracture, limb length discrepancies,bone growth abnormalities and nerve lesions. Neurologic involvement, ranging from sensory and motor nerve palsies to complete hand paralysis, may persist.

Поширеність
<1 / 1 000 000
Вік початку
Neonatal