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Муцинозна цистаденокарцинома підшлункової залози

ORPHA:424053· ICD-10 C25.2· Mucinous cystadenocarcinoma of the pancreas

Визначення(English summary)

A rare, epithelial tumor of the pancreas characterized, histologically, by columnar, mucin-producing epithelium associated with ovarian-type subepithelial stroma, which does not communicate with the pancreatic ductal system, most frequently localized to the body or tail of the pancreas. Clinically, small tumors (<3 cm) are usually asymptomatic, while large tumors typically present obstructive jaundice, a palpable abdominal mass, and may associate portal hypertension, hemobilia and diabetes mellitus.

Поширеність
<1 / 1 000 000
Успадкування
Not applicable
Вік початку
Adult