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Плеоморфна ксантоастроцитома

ORPHA:251607· ICD-10 C71.9· Pleomorphic xanthoastrocytoma

Визначення(English summary)

A rare low-grade astrocytoma characterized by superficial location in the cerebral hemispheres with involvement of the meninges, composed of GFAP-expressing cells showing nuclear and cytoplasmic pleomorphism and xanthomatous change, surrounded by a reticulin network. The tumor corresponds to WHO grade II and typically affects children and young adults, who often present with a long history of seizures. Extent of resection and mitotic index are important prognostic factors.

Поширеність
<1 / 1 000 000
Успадкування
Not applicable
Вік початку
All ages