Плеоморфна ксантоастроцитома
ORPHA:251607· ICD-10 C71.9· Pleomorphic xanthoastrocytoma
Визначення(English summary)
A rare low-grade astrocytoma characterized by superficial location in the cerebral hemispheres with involvement of the meninges, composed of GFAP-expressing cells showing nuclear and cytoplasmic pleomorphism and xanthomatous change, surrounded by a reticulin network. The tumor corresponds to WHO grade II and typically affects children and young adults, who often present with a long history of seizures. Extent of resection and mitotic index are important prognostic factors.
- Поширеність
- <1 / 1 000 000
- Успадкування
- Not applicable
- Вік початку
- All ages