Синдром Дубіна-Джонсона
ORPHA:234· ICD-10 E80.6· Dubin-Johnson syndrome
Визначення(English summary)
Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.
- Поширеність
- Unknown
- Успадкування
- Autosomal recessive
- Вік початку
- Adolescent, Adult