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Первинна шкірна агресивна епідермотропна CD8+ Т-клітинна лімфома

ORPHA:178528· ICD-10 C84.5· Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma

Визначення(English summary)

Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma is a rare form of primary cutaneous T-cell lymphoma characterized by rapidly progressing, localized or disseminated nodules, tumors or eczematous skin lesions. It has a particularly aggressive clinical course with a high tendency to spread, in advanced stages, to extracutaneous locations (the central nervous system, lung, testes). Lymph nodes are often spared.