Набутий гемофагоцитарний лімфогістіоцитоз, повязаний зі злоякісними захворюваннями
ORPHA:158057· ICD-10 D76.1· Acquired hemophagocytic lymphohistiocytosis associated with malignant disease
Визначення(English summary)
A rare, secondary hemophagocytic lymphohistiocytosis characterized by occurring as either initial presentation of a malignant disease or at any stage during chemotherapy. The common associated malignancies are lukemias, B-cell, T-cell or NK-cell lymphomas, and Hodgkin lymphoma. Typical clinical manifestation includes fever, hepatosplenomegaly and cytopenias, combined with specific laboratory findings.
- Поширеність
- Unknown
- Вік початку
- All ages