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ORPHA:137605· ICD-10 Q85.0· Legius syndrome

Визначення(English summary)

Legius syndrome, also known as NF1-like syndrome, is a rare, genetic skin pigmentation disorder characterized by multiple café-au-lait macules with or without axillary or inguinal freckling.

Поширеність
1-9 / 100 000
Успадкування
Autosomal dominant
Вік початку
Childhood, Infancy, Neonatal