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Wiskott-Aldrich syndrome

ORPHA:906· ICD-10 D82.0

Definition

A primary immunodeficiency disease characterized by microthrombocytopenia, eczema, infections and an increased risk for autoimmune manifestations and malignancies.

Prevalence
1-9 / 1 000 000
Inheritance
Autosomal dominant, Autosomal recessive, Not applicable, X-linked recessive
Age of onset
Infancy, Neonatal