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Congenital insensitivity to pain-anosmia-neuropathic arthropathy

ORPHA:88642· ICD-10 G60.8

Definition

A rare genetic peripheral neuropathy characterized by complete congenital insensitivity to painful stimuli, commonly associated with neuropathic arthropathy. In addition, patients are typically anosmic.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant, Autosomal recessive
Age of onset
Neonatal