vitalwiki

Central areolar choroidal dystrophy

ORPHA:75377· ICD-10 H31.2

Definition

A hereditary macular disorder, usually presenting between the ages of 30-60, characterized by a large area of atrophy in the centre of the macula and the loss or absence of photoreceptors, retinal pigment epithelium and choriocapillaris in this area, resulting in a progressive decrease in visual acuity.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant
Age of onset
Adult