vitalwiki

Hereditary spastic paraplegia

ORPHA:685· ICD-10 G11.4

Definition

A genetically and clinically heterogeneous group of slowly progressive neurological disorders which in the pure form is characterized by pyramidal signs (weakness, spasticity, brisk tendon reflexes, and extensor plantar responses) predominantly affecting the lower limbs and with possible association of sphincter disturbances and deep sensory loss; and in the complex form by the addition of variable neurological or non-neurological features.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant, Autosomal recessive, X-linked recessive
Age of onset
All ages