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Euthyroid dysprealbuminemic hyperthyroxinemia

ORPHA:597939· ICD-10 E07.8

Definition

A rare genetic endocrine disease characterized by increased affinity of a mutated transthyretin for T4. Total and free T4 may be normal or elevated, but affected individuals are clinically euthyroid.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Adult