Congenital short QT syndrome
ORPHA:51083· ICD-10 I49.8
Definition
A rare, genetic cardiac rhythm disease characterized by a short QTc interval on the surface electrocardiogram (ECG) with a high risk of syncope or sudden death due to malignant ventricular arrhythmia.
- Prevalence
- Unknown
- Inheritance
- Autosomal dominant
- Age of onset
- All ages