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Familial benign flecked retina

ORPHA:363989· ICD-10 H35.5

Definition

Familial benign flecked retina is a rare retinal dystrophy characterized by diffuse bilateral white-yellow fleck-like lessions extending to the far periphery of the retina but sparing the foveal region, with asymptomatic clinical phenotype and absence of electrophysiologic deficits.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Adult, Childhood