vitalwiki

Stormorken-Sjaastad-Langslet syndrome

ORPHA:3204· ICD-10 D69.8

Definition

Stormorken-Sjaastad-Langslet syndrome is characterized by thrombocytopathy, asplenia, miosis, muscle fatigue, migraine, dyslexia, and ichthyosis. It has been described in six members of one family. It is transmitted as an autosomal dominant trait.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
All ages