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Pelizaeus-Merzbacher disease, connatal form

ORPHA:280210· ICD-10 E75.2

Definition

The connatal form of Pelizaeus-Merzbacher disease (PMD) is the most severe form of PMD.

Prevalence
<1 / 1 000 000
Inheritance
X-linked recessive
Age of onset
Infancy, Neonatal