vitalwiki

COG5-CDG

ORPHA:263487· ICD-10 E77.8

Definition

COG5-CDG is an extremely rare form of CDG syndrome characterized clinically in the single reported case to date by moderate mental retardation with slow and inarticulate speech, truncal ataxia, and mild hypotonia.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal recessive
Age of onset
Childhood