vitalwiki

Prominent glabella-microcephaly-hypogenitalism syndrome

ORPHA:2083· ICD-10 Q87.8

Definition

A rare syndrome described and characterized by prenatal onset of growth deficiency, microcephaly, hypoplastic genitalia, and birth onset of convulsions.

Prevalence
<1 / 1 000 000
Age of onset
Antenatal, Neonatal