vitalwiki

葡糖-6-磷酸酶缺乏所致糖原贮积症1b型

ORPHA:79259· ICD-10 E74.0· Glycogen storage disease due to glucose-6-phosphatase deficiency type Ib

患病率
Unknown
遗传方式
Autosomal recessive
发病年龄
Infancy, Neonatal