Тотальний аномальний дренаж легеневих вен
ORPHA:99125· ICD-10 Q26.2· Congenital total pulmonary venous return anomaly
Визначення(English summary)
A form of congenital pulmonary venous return where all of the pulmonary veins drain into the right atrium or one of its tributaries, instead of the left atrium, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and progressive congestive heart failure.
- Поширеність
- 1-9 / 100 000
- Успадкування
- Not applicable
- Вік початку
- Neonatal