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Мявий системний мастоцитоз

ORPHA:98848· ICD-10 D47.0· Indolent systemic mastocytosis

Визначення(English summary)

A rare, usually benign, chronic, form of systemic mastocytosis (SM) characterized by an abnormal accumulation of neoplastic mast cells (MCs) mainly in the bone marrow (BM) but also in other organs or tissues such as preferably the skin.

Поширеність
1-5 / 10 000
Успадкування
Not applicable
Вік початку
Adult, Elderly