Мявий системний мастоцитоз
ORPHA:98848· ICD-10 D47.0· Indolent systemic mastocytosis
Визначення(English summary)
A rare, usually benign, chronic, form of systemic mastocytosis (SM) characterized by an abnormal accumulation of neoplastic mast cells (MCs) mainly in the bone marrow (BM) but also in other organs or tissues such as preferably the skin.
- Поширеність
- 1-5 / 10 000
- Успадкування
- Not applicable
- Вік початку
- Adult, Elderly