Мультилокулярна кіста нирки
ORPHA:97366· ICD-10 D30.0· Multiloculated renal cyst
Визначення(English summary)
A rare benign renal tumor characterized by a typically unilateral, solitary, multiloculated cystic mass consisting of small, non-communicating cysts with flat, cuboidal, or hobnail epithelial lining, separated by fibrous septa which may have an ovarian stroma-like appearance or be paucicellular. The tumor is surrounded by a thick fibrous capsule and does not contain solid areas or necrosis. Patients may be asymptomatic or present with a palpable abdominal mass and/or abdominal or flank pain. Age distribution is bimodal, the typical age of onset being either below five or between 40 and 70 years of age.
- Поширеність
- Unknown
- Вік початку
- Adult, Elderly, Infancy