Печінкова венооклюзивна хвороба
ORPHA:890· ICD-10 K76.5· Hepatic veno-occlusive disease
Визначення(English summary)
A rare vascular liver disease characterized by toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins and sinusoids. Clinical manifestations include painful hepatomegaly, jaundice, and fluid retention that manifests by weight gain, edemas, and ascites.
- Поширеність
- Unknown
- Успадкування
- Not applicable
- Вік початку
- All ages