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Печінкова венооклюзивна хвороба

ORPHA:890· ICD-10 K76.5· Hepatic veno-occlusive disease

Визначення(English summary)

A rare vascular liver disease characterized by toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins and sinusoids. Clinical manifestations include painful hepatomegaly, jaundice, and fluid retention that manifests by weight gain, edemas, and ascites.

Поширеність
Unknown
Успадкування
Not applicable
Вік початку
All ages